Systemic mastocytosis in association with chronic lymphocytic leukemia: A rare diagnosis

Patricia Ault, Alice Lynn, Constantine S. Tam, L. Jeffrey Medeiros, Michael J. Keating

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12 Citations (Scopus)

Abstract

Systemic mastocytosis may be primary or be associated with other hematological malignancies, most commonly myeloid neoplasms. In contrast, the association of systemic mastocytosis with lymphoid neoplasms is comparatively rare, and in the absence of appropriate clinical vigilance the diagnosis may be missed. We report a case of aggressive systemic mastocytosis associated with chronic lymphocytic leukemia (SM-CLL), placing particular emphasis on the investigational algorithm used in establishing this diagnosis, and discussing key clinical considerations in the initiation of therapy.

Original languageEnglish
Pages (from-to)1755-1758
Number of pages4
JournalLeukemia Research
Volume31
Issue number12
DOIs
Publication statusPublished - Dec 2007
Externally publishedYes

Keywords

  • Alemtuzumab
  • Imatinib
  • Lymphoproliferative diseases
  • Myeloproliferative disease

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