Contemporary advances in antibody-mediated encephalitis: anti-LGI1 and anti-Caspr2 antibody (Ab)-mediated encephalitides

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Abstract

Encephalitides with antibodies directed against leucine-rich glioma-inactivated 1 (LGI1) and contactin-associated protein-like 2 (Caspr2) represent two increasingly well characterised forms of autoimmune encephalitis. Both share overlapping and distinct clinical features, are mediated by autoantibodies directed against differing proteins complexed with voltage-gated potassium channels, with unique genetic predisposition identified to date. Herein we summarise disease mechanisms, clinical features, treatment considerations, prognostic factors and clinical outcomes regarding these disorders.

Original languageEnglish
Article number103074
Number of pages12
JournalAutoimmunity Reviews
Volume21
Issue number5
DOIs
Publication statusPublished - May 2022

Keywords

  • Anti-contactin-associated protein-like 2 (Caspr2) encephalitis
  • Anti-leucine-rich glioma-inactivated-1 (LGI1) encephalitis
  • LGI1-, Caspr2-encephalitis pathogenesis, clinical features, management
  • LGI1-, Caspr2-encephalitis prognostic features, outcomes

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