cANCA-associated aortitis

Liv A. Amos, Matthew A. Roberts, Susan Blair, Lawrence P. McMahon

Research output: Contribution to journalArticleOtherpeer-review

8 Citations (Scopus)

Abstract

Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis is traditionally viewed as a small vessel disease. We report a patient with cANCA antibodies directed against proteinase-3 with asymptomatic aortic involvement, in combination with diffuse alveolar haemorrhage and pauci-immune, necrotizing crescentic glomerulonephritis. A review of the literature is discussed.

Original languageEnglish
Pages (from-to)47-49
Number of pages3
JournalClinical Kidney Journal
Volume5
Issue number1
DOIs
Publication statusPublished - 2012

Keywords

  • aortitis
  • cANCA
  • vasculitis
  • Wegener's granulomatosis

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