Bilateral keratocystic odontogenic tumor of mandible - A unique pediatric lesion: Case report and review

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The keratocystic odontogenic tumor (KCOT) is the most common cystic neoplasm in the maxillofacial region. Multiple odontogenic keratocyst are usually associated with Nevoid Basal Cell Carcinoma (NBCC) syndrome. A variant of this neoplasm is the sporadic multiple KCOT in pediatric population. Presented here is a case of bilateral keratocystic odontogenic tumor in a fourteen year old. Multiple keratocysts in the pediatric population is rare, aggressive, and recurrent and the first sign of NBCC or the solo presentation of human homologue of the PTCH (Drosophila segment polarity gene Patched) gene mutation.

Original languageEnglish
Pages (from-to)140-143
Number of pages4
JournalInternational Journal of Pediatric Otorhinolaryngology Extra
Issue number4
Publication statusPublished - Dec 2013
Externally publishedYes


  • Juvenile
  • Keratocystic odontogenic tumor
  • Neoplasm
  • Nevoid Basal Cell Carcinoma syndrome

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