TY - JOUR
T1 - Anesthetic management of a myotonic dystrophy patient with paraganglionoma
AU - Subramaniam, Ashwin
AU - Grauer, Robert
AU - Beilby, David
AU - Tiruvoipati, Ravindranath
N1 - Publisher Copyright:
Crown Copyright © 2016 Published by Elsevier Inc. All rights reserved.
PY - 2016/11/1
Y1 - 2016/11/1
N2 - Myotonic dystrophy (DM), though rare, can significantly complicate anesthesia due to muscular and extra-muscular involvement. When this condition is compounded by a pheochromocytoma, anesthetizing such patients becomes extra challenging. We present a case report of a 61-year-old lady with congenital DM, with the whole gamut of associated features, was diagnosed with a noradrenaline secreting paraganglionoma following investigation of refractory hypertension. We anesthetized her for an open resection of the lesion. The conduct of anesthesia and recovery of this patient is described. Our experience suggests that anesthetizing these patients though challenging can be safely managed with relaxant general anesthesia and epidural analgesia with meticulous care pre, intra and post-surgical intervention.
AB - Myotonic dystrophy (DM), though rare, can significantly complicate anesthesia due to muscular and extra-muscular involvement. When this condition is compounded by a pheochromocytoma, anesthetizing such patients becomes extra challenging. We present a case report of a 61-year-old lady with congenital DM, with the whole gamut of associated features, was diagnosed with a noradrenaline secreting paraganglionoma following investigation of refractory hypertension. We anesthetized her for an open resection of the lesion. The conduct of anesthesia and recovery of this patient is described. Our experience suggests that anesthetizing these patients though challenging can be safely managed with relaxant general anesthesia and epidural analgesia with meticulous care pre, intra and post-surgical intervention.
KW - dystrophia myotonica
KW - general anesthesia
KW - hypertension
KW - Myotonic dystrophy
KW - paraganglionoma
KW - pheochromocytoma
UR - http://www.scopus.com/inward/record.url?scp=84964614629&partnerID=8YFLogxK
U2 - 10.1016/j.jclinane.2016.03.035
DO - 10.1016/j.jclinane.2016.03.035
M3 - Article
C2 - 27687340
AN - SCOPUS:84964614629
VL - 34
SP - 21
EP - 28
JO - Journal of Clinical Anesthesia
JF - Journal of Clinical Anesthesia
SN - 0952-8180
ER -